Tumores de partes moles AULA UFPA 2014
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Transcript of Tumores de partes moles AULA UFPA 2014
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Tumores de Partes Moles
Prof. Msc. José Abreu Jr
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Tumores de Partes Moles
• Neoplasias oriundas de tecidos de origem
mesodérmica extra-esqueléticos.
1-Conjuntivo Fibroso.
2-Musculo Liso.
3-Tecido Adiposo.
4-Nervos periféricos.
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Princípios Diagnósticos Gerais
---Localização.
Tumores profundos tendem a ser malignos,
tumores superficiais, tendem a ser benignos.
---Tamanho.
Tumores maiores tendem a ser malignos.
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---Padrão de crescimento.
Rápido e infiltrativo, sugere malignidade.
---Metástase.
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Tumores de Partes Moles
• Abordagem diagnóstica.
---Histologia.
---Imuno-Histoquímica.
---Estudos Citogenéticos.
---Análise Molecular.
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BENIGNO X MALIGNOcelularidade
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BENIGNO X MALIGNOatipias nucleocitoplasmáticas
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BENIGNO X MALIGNOatipias nucleocitoplasmáticas
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Tumores de Partes Moles
t( 2:13) Alveolar rhabdomyosarcoma
t( 11;22) Ewing’s sarcoma/PNET
t( 11;22) Desmoplastic small round cell tumor
t( 12;16) Myxoid liposarcoma
t( 9;22) Myxoid chondrosarcoma
t(12;22) Clear cell sarcoma
t( X;18) Synovial sarcoma
Alterações Citogenéticas
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Lesões Pseudotumorais
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Fasciite Nodular
Lesão de caráter reativo (benigna)
Provavelmente secundária a trauma.
Ombros, tronco, costa. Bem delimitada.
Células Fusiformes ( fibroblastos & miofibroblastos)
Crescimento rápido, frequentes mitoses.
Auto-limitada, cura por excisão.
Deve ser diferenciada de sarcomas.
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Fasciite Nodular
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Fibromatose
Lesão Fibroproliferativa.
Aspecto de massa infiltrativa.
Fibroblastos e miofibroblastos.
Fibromatose palmar, plantar.
Excisão cirúrgica.
Padrão de crescimento infiltrativo.
Tendência a reicidiva.
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Fibromatosis
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Tumores
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Fibrossarcoma
Tumor maligno de origem fibroblástica.
Mais em adultos, no tronco e nos MMII
e MMSS.
Aumento da celularidade e perda da relação
Núcleo citoplasmática.
Células fusiformes com padrão em espinha de peixe
Diagnósticos diferenciais.
- Tumores da bainha do nervo periférico
- Sarcoma Sinovial
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Fibrossarcoma
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Dermatofibroma
Fibro Histiocitoma benigno.
Tumor de pele
Mistura de fibroblastos, miofibroblastos
e histiócitos.
Excisão cirúrgica.
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Dermatofibroma
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Dermatofibrossarcoma
Protuberans (DFSP)
Tumor fibrohistiocitário
Potêncial maligno intermediário.
Pele e subcutâneo.
Céls. Fusocelulares em padrão estoriforme
Reicidiva local
CD 34
Transformação em fibrossarcoma.
Excisão cirúrgica.
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Dermatofibrossarcoma Protuberans ( DFSP )
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Fibro Histiocitoma Maligno
Tumor maligno de partes moles com diferen
ciação fibro histiocitária.
Tipo mais comum de sarcoma de partes moles
Mais frequente sarcoma pós-radioterapia
Adultos, partes moles profundas, extremidades e
retroperitôneo.
Marcado pleomorfismo, células fusiformes,
estoriformes, áreas mixóides.
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MFH
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Leiomioma
Tumor benigno de partes moles.
Feixes regulares de células musculares lisas
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Leiomioma
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Leiomiossarcoma
Tumor maligno de partes moles.
Surge nas extremidades da parede dos
vasos.
Necrose, hemorragia.
Feixes celulares com atipias nucleares.
Alta atividade mitótica.
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Leiomiossarcoma
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Rabdomiossarcoma
Tumor maligno do músculo estriado.
Comum em crianças e adultos jovens.
Alguns subtipos
- Embrionário
- Alveolar
- Botrióide
- Pleomorfico
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Rabdomiossarcoma
Embrionário
Mais comum em crianças na cabeça e
pescoço.
Subtipo mais comum.
Rabdomioblastos com
estriações citoplasmáticas.
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Rabdomiossarcoma Embrionário
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Rabdomiossarcoma
Botrióide
Mais comum no trato genitourinário
Paredes de órgãos cavitários.
Massas tumorais polipóides como cachos
de uva. Células malignas em um estroma mixóide.
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Rabdomiossarcoma Botrióide
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Rabdomiossarcoma
Alveolar
Nas extremidades
Septos fibrosos com feixes de células
Redondas no centro.
- Padrão alveolar.
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Rabdomiossarcoma Alveolar
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Rabdomiossarcoma
Pleomórfico
Musculos esqueléticos de pessoas
idosas.
Acentuado pleomorfimso.
Arranjos celulares irregulares.
Células gigantes multinucleadas.
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Sarcoma Pleomórfico
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Lipoma
Benigno, tumor circunscrito de
adipócitos maduros.
Usualmente subcutâneo, mas pode
aparecer onde houver tecido adiposo.
Tipo mais comum de tumor
benigno de partes moles.
No adulto, ombros, pescoço.
Parece tecido adiposo normal.
Vários subtipos: Angiolipoma, Lipoma de
células fusiformes.
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Lipoma
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Lipossarcoma
Segundo sarcoma mais comum em adultos
Em áreas profundas das extremidades e
retroperitôneo.
Lipoblastos.
Varios subtipos
-Bem diferenciado, tumor
lipomatoso atípico.
- Mixóide / Células Redondas
- Pleomórfico.
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Lipossarcoma
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Hemangioma
Lesão benigna
Lembra vasos normais.
Congenita ou não congenita.
Mais comum em crianças.
Cabeça, pescoço, orgãos internos -
Fígado
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Angiossarcoma
Tumor maligno vascular.
Muitas localizações: pele, partes moles,
mama, baço, fígado.
Vasos com lumem irregular e endotélio
atípico.
CD31- marcador de células endoteliais.
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Angiossarcoma
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Schwannoma
Tumor benigno de diferenciação neural.
- Celúlas de Schwann cells
Antoni A
Antoni B
Sempre associado a filetes nervosos.
Cabeça, pescoço e extremidades.
-- Área celular, núcleo em paliçada
-- Área menos celular, fundo mixóide.
S-100
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Schwannoma
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Sarcoma Sinovial
Tumor maligno de partes moles.
Surgimento em partes moles profundas
Origem desconhecida.
Multilobular
Padrão bifásico.
- Células fusiformes.
- Células epitelioides.
t( X;18 )
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Sarcoma Sinovial
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Questões que devem ser
resolvidas pelo patologista1. A lesão é tumoral ou reativa?
2. É benigna ou maligna?
3. Se é maligna, é um sarcoma ou uma malignidade que imita um sarcoma?
4. Se é um sarcoma, qual é o grau
5. Qual o tipo histológico do tumor (benigno ou maligno)?
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